As a result of the revision and discussion of the RHD-DGs during the Board of the Network meeting (13-14 November 2019, Barcelona), a total of 70 RHD-DG has been identified. The Lymphoid malignancies subnetwork includes 19 disease groups encompassing 98 disorders.
RHD-DGs and disorders included are currently under revision for final approval.
Disease Group | Disorders included |
---|---|
Acute lymphoblastic leukemia | Precursor B-cell acute lymphoblastic leukemia |
Precursor T-cell acute lymphoblastic leukemia | |
Diffuse large B-cell lymphoma, Other than NOS | Plasmablastic lymphoma |
Primary effusion lymphoma | |
Large B-cell lymphoma with IRF4 rearrangement* | |
T-cell/histiocyte-rich large B-cell lymphoma | |
Primary DLBCL of the central nervous system (CNS) | |
Primary cutaneous DLBCL, leg type | |
EBV+ mucocutaneous ulcer* | |
DLBCL associated with chronic inflammation | |
Lymphomatoid granulomatosis | |
Primary mediastinal (thymic) large B-cell lymphoma | |
Intravascular large B-cell lymphoma | |
ALK+ large B-cell lymphoma | |
Diffuse large B-cell lymphoma, NOS | EBV+ DLBCL, NOS* |
HHV8+ DLBCL, NOS* | |
Diffuse large B-cell lymphoma (DLBCL), NOS | |
Diffuse large B-cell lymphoma (DLBCL), NOS | |
Follicular lymphoma | In situ follicular neoplasia* |
Duodenal-type follicular lymphoma* | |
Primary cutaneous follicle center lymphoma | |
Hairy cell leukemia | Hairy cell leukemia |
Histiocytic and dendritic cell neoplasms | Histiocytic sarcoma |
Langerhans cell histiocytosis | |
Langerhans cell sarcoma | |
Indeterminate dendritic cell tumor | |
Interdigitating dendritic cell sarcoma | |
Follicular dendritic cell sarcoma | |
Fibroblastic reticular cell tumor | |
Disseminated juvenile xanthogranuloma | |
Erdheim-Chester disease* | |
Hodgkin lymphoma | Nodular lymphocyte predominant Hodgkin lymphoma |
Classical Hodgkin lymphoma | |
Classical Hodgkin lymphoma nodular sclerosis type | |
Classical Hodgkin lymphoma mixed cellularity type | |
Classical Hodgkin lymphoma lymphocyte-rich type | |
Classical Hodgkin lymphoma lymphocyte-depleted type | |
Chronic lymphocytic leukemia/small lymphocytic lymphoma | |
Monoclonal B-cell lymphocytosis* | |
B-cell prolymphocytic leukemia | |
Splenic marginal zone lymphoma | |
Indolent B-cell lymphomas / Non Follicular | Splenic B-cell lymphoma/leukemia, unclassifiable |
Splenic B-cell lymphoma/leukemia, unclassifiable | |
Lymphoplasmacytic lymphoma | |
Lymphoplasmacytic lymphoma | |
MALT lymphoma | |
Nodal marginal zone lymphoma | |
Mantle cell lymphoma | Mantle cell lymphoma |
Mature T-cell neoplasms non primary cutaneous.1 Leukemic | Chronic lymphoproliferative disorder of NK cells |
T-cell prolymphocytic leukemia | |
T-cell large granular lymphocytic leukemia | |
Aggressive NK-cell leukemia | |
Adult T-cell leukemia/lymphoma | |
Mature T-cell neoplasms non primary cutaneous.2 Extra nodal | Enteropathy-associated T-cell lymphoma |
Monomorphic epitheliotropic intestinal T-cell lymphoma* | |
Breast implant-associated anaplastic large-cell lymphoma* | |
Extranodal NK-/T-cell lymphoma, nasal type | |
Indolent T-cell lymphoproliferative disorder of the GI tract* | |
Hepatosplenic T-cell lymphoma | |
Mature T-cell neoplasms non primary cutaneous.2 Nodal | Peripheral T-cell lymphoma, NOS |
Angioimmunoblastic T-cell lymphoma | |
Anaplastic large-cell lymphoma, ALK+ | |
Anaplastic large-cell lymphoma, ALK−* | |
Nodal peripheral T-cell lymphoma with TFH phenotype* | |
Follicular T-cell lymphoma* | |
Subcutaneous panniculitis-like T-cell lymphoma | |
Mycosis fungoides | |
Sézary syndrome | |
Primary cutaneous CD30+ T-cell lymphoproliferative disorders | |
Mature T-cell neoplasms primary cutaneous | Primary cutaneous CD30+ T-cell lymphoproliferative disorders |
Primary cutaneous γδ T-cell lymphoma | |
Primary cutaneous CD8+ aggressive epidermotropic cytotoxic T-cell lymphoma | |
Primary cutaneous acral CD8+ T-cell lymphoma* | |
Primary cutaneous CD4+ small/medium T-cell lymphoproliferative disorder* | |
Other agressive B-cell neoplasms | Burkitt lymphoma |
Burkitt-like lymphoma with 11q aberration* | |
High-grade B-cell lymphoma, with MYC and BCL2 and/or BCL6 rearrangements* | |
High-grade B-cell lymphoma, NOS* | |
B-cell lymphoma, unclassifiable, with features intermediate between DLBCL and classical Hodgkin lymphoma | |
Monoclonal gammopathy of undetermined significance (MGUS), IgM* | |
μ heavy-chain disease | |
γ heavy-chain disease | |
α heavy-chain disease | |
Monoclonal gammopathy of undetermined significance (MGUS), IgG/A* | |
Plasma cell neoplasm | Solitary plasmacytoma of bone |
Extraosseous plasmacytoma | |
Monoclonal immunoglobulin deposition diseases* | |
POEMS syndrome | |
Plasma cell leukemia | |
Plasma cell myeloma (not rare) | Plasma cell myeloma |
AL amyloidosis | AL amyloidosis |
Posttransplant lymphoproliferative disorders (PTLD) | Plasmacytic hyperplasia PTLD |
Infectious mononucleosis PTLD | |
Florid follicular hyperplasia PTLD* | |
Polymorphic PTLD | |
Monomorphic PTLD (B- and T-/NK-cell types) | |
Classical Hodgkin lymphoma PTLD |